Pulmonary veno-occlusive disease
Definition
Pulmonary veno-occlusive disease is an extremely rare form of high blood pressure in the lung area (primary pulmonary hypertension).
Alternative Names
Pulmonary vaso-occlusive disease
Causes
In most cases, the cause of pulmonary veno-occlusive disease is unknown. The condition may be related to a viral infection. It may occur as a complication of certain diseases such as lupus, or as a complication of leukemia, lymphoma, or chemotherapy.
The disorder is most common among children and young adults. As the disease gets worse, it causes narrowed pulmonary veins, pulmonary hypertension, congestion, and edema (swelling) of the lungs.
References
Zipes DP, Libby P, Bonow RO, Braunwald E, eds. Braunwald's Heart Disease: A Textbook of Cardiovascular Medicine, 7th ed. St. Louis, Mo; WB Saunders; 2005:829.
Mason RJ, Murray J, VC Broaddus, Nadel J. Murray & Nadel's Textbook of Respiratory Medicine. 3rd ed. Philadelphia, Pa: WB Saunders; 2000:1472-1473.
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