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Tricuspid atresia

Definition

Tricuspid atresia is a type of congenital heart disease in which the tricuspid heart valve is missing or abnormally developed. The defect blocks blood flow from the right atrium to the right ventricle.

Alternative Names

Tri atresia

Causes

Tricuspid atresia is an uncommon form of congenital heart disease that affects about 5 in every 100,000 live births. Twenty percent of patients with this condition will have also have other heart problems.

Normally, blood flows into the right atrium, then through the tricuspid valve to the right ventricle and on to the lungs. If the tricuspid valve is missing or broken, the blood cannot flow from the right atrium to the left ventricle. Blood ultimately cannot enter the lungs, where it must go to pick up oxygen (become oxygenated).

Infants with tricuspid atresia generally are cyanotic (bluish discoloration of skin) and easily become short of breath.

References

Zipes DP, Libby P, Bonow RO, Braunwald E, eds. Braunwald's Heart Disease: A Textbook of Cardiovascular Medicine, 8th ed. St. Louis, Mo; WB Saunders; 2007.

Review Date: 12/10/2007
Reviewed By: David Zieve, MD, MHA, Medical Director, A.D.A.M., Inc.; and Mark A Fogel, MD, FACC, FAAP, Associate Professor of Pediatrics and Radiology, Director of Cardiac MR, The Children's Hospital of Philadelphia.

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