Baylor Health Care System
 

Hallervorden-Spatz disease

Definition

Hallervorden-Spatz disease is a movement disorder that is passed down through families (inherited).

Causes

Hallervorden-Spatz is a disease that slowly gets worse (is degenerative). It usually begins in childhood. The condition involves muscle rigidity, weakness, and movement problems.

Most cases of Hallervorden-Spatz are due to a defect in a gene that makes a protein called pantothenate kinase 2. Patients with this genetic defect have a build up of iron in parts of the brain, especially the basal ganglia.

Review Date: 8/26/2006
Reviewed By: Gail A. Kang, M.D., San Francisco VA Parkinson's Disease Research, Education, & Clinical Center, San Francisco, CA. Review provided by VeriMed Healthcare Network.

A.D.A.M., Inc. is accredited by URAC, also known as the American Accreditation HealthCare Commission. URAC's accreditation program is the first of its kind, requiring compliance with 53 standards of quality and accountability, verified by independent audit.

The information provided herein should not be used during any medical emergency or for the diagnosis or treatment of any medical condition. A licensed medical professional should be consulted for diagnosis and treatment of any and all medical conditions. Call 911 for all medical emergencies. Links to other sites are provided for information only -- they do not constitute endorsements of those other sites. Copyright 2005 A.D.A.M., Inc. Any duplication or distribution of the information contained herein is strictly prohibited.